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Loss of Nuclear Envelope Integrity and Increased Oxidant Production Cause DNA Damage in Adult Hearts Deficient in PKP2: A Molecular Substrate of ARVC | Circulation
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Genes | Free Full-Text | Clinical and Molecular Data Define a Diagnosis of Arrhythmogenic Cardiomyopathy in a Carrier of a Brugada-Syndrome-Associated PKP2 Mutation
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Plakophilin-2 is required for transcription of genes that control calcium cycling and cardiac rhythm | Nature Communications
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Progressive Reduction in Right Ventricular Contractile Function Attributable to Altered Actin Expression in an Aging Mouse Model of Arrhythmogenic Cardiomyopathy | Circulation
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Novel frame-shift mutation in PKP2 associated with arrhythmogenic right ventricular cardiomyopathy: a case report | BMC Medical Genetics | Full Text
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Plakophilin 2 structure and locations of ARVC mutations. A sequence... | Download Scientific Diagram
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Plakophilin-2 truncating variants impair cardiac contractility by disrupting sarcomere stability and organization | Science Advances
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